Williams Syndrome (WS), aka Williams Beuren Syndrome, is a developmental disorder that we have known about for some forty years. The cause for WS was detected only recently: a micro deletion on chromosome 7, more specifically at the region of chromosome 7q11.23. The cognitive and behavioral profile in WS is characterized by a marked discrepancy between verbal and non-verbal skills combined with relatively spared linguistic skills. Recent research has shown considerable progress defining the areas of intactness in linguistic abilities. This volume builds on that research, giving an overview of the psycholinguistic research undertaken and opening up new perspectives and insights through new data and analyses. This book is of interest to researchers of applied cognitive science and to linguists more occupied with theoretical research.

Updated and expanded to 124 entries, The Cambridge Encyclopedia of Child Development remains the authoritative reference in the field.

A blueprint for the investigation of neurodevelopmental disorders, this book presents the work of a team of scientists using a multidisciplinary, integrated approach to link genes with human behavior. Using Williams syndrome as a model, leading researchers in neuroanatomy, neurocognition, neurophysiology, and molecular genetics have built bridges between disciplines to link higher cognitive functions, their underlying neurobiological bases, and their molecular genetic underpinnings. One of the book's many strengths is that the scientists from each discipline studied the same individuals with Williams syndrome. As the book shows, Williams syndrome is a fascinating disorder because of the "peaks and valleys" among cognitive domains: severe intellectual deficits but remarkably spared and effusive language; specific impairment in spatial construction but great strength in face processing and sociability. By capitalizing on these dissociations in higher cognitive functioning, the book provides a model for the study of brain-behavior relationships as well as for the mapping of brain and behavior phenotypes to the genome and beyond. Contributors Ralph Adolphs, Twyla Alvarez, Lawrence Appelbaum, Ursula Bellugi, Dennis Burian, Xiao-Ning Chen, Michael Chiles, Stephan Eliez, Albert Galaburda, Hanao Hirota, Wendy Jones, Julie Korenberg, Zona Lai, Liz Lichtenberger, Alan Lincoln, Rumiko Matsuoka, Debra Mills, Helen Neville, Judy Reilly, Allan Reiss, Bruce Roe, Marie St. George, J. Eric Schmidtt, Erica Straus

Language as a connecting bridge between learning disability and psychiatric disorder is the unifying theme of this wide-ranging book. Particular prominence is given to attention deficit hyperactivity disorder, dyslexia and autistic disorder. Explanations for the comorbidity of psychiatric and language disorder are sought in developmental, cognitive and biological fields, the contribution of imaging modalities is considered and implications for aetiology, treatment and rehabilitation are explored. Topical issues such as syndrome definition in dyslexia, acquired memory disorder in childhood and biology-behaviour correspondence are well covered, as are a range of treatment options. A final section is devoted to outcome studies. Enlivened with case vignettes, and offering insights into the range of current thinking on language and behaviour, this book is a rich resource for professionals and advanced students concerned with child health and development, offering ideas for a unified view of language, learning and behaviour problems.

Comprehensive and readable, Understanding Williams Syndrome: Behavioral Patterns and Interventions is an essential guide for all those professionally, scientifically, or personally involved with this so frequently misunderstood and underserved population--psychologists, psychiatrists, social workers, and other mental health professionals; special educators and vocational counselors; speech-language, physical, and occupational therapists; audiologists; physicians; and parents. In the last 20 years, Williams syndrome has captured the interest of large numbers of scientists and attracted considerable media attention in spite of its rarity (estimated at no more than one in 30,000 births). Those diagnosed display a unique pattern of behavioral, cognitive, and physical limitations and strengths with fascinating neurogenetic implications--a pattern that poses enormous challenges to their parents and caregivers. The authors, a specialist in learning disabilities and a developmental psychologist, review basic information about Williams syndrome, its medical conditions, paradoxical profile, and neurobiological mechanisms; and discuss distinctive features of the language and perceptual and motor performance of children and adults with the syndrome. Other features include: * Strategies for working with patients. * An examination of the difference between Williams syndrome and other developmental disorders. * Problem-specific alternatives for treatment. * Analysis of new directions in research, clinical intervention, education, and systems for care delivery. Throughout, they stress variations among individuals and subgroups in ability level, skills, talents, and problem severity; and emphasize the necessity of recognizing these components in planning treatment on an individual basis.

This book presents a range of ongoing studies on atypical language development in Romance languages. Despite the steady increase in the number of studies on typical language development, there is still little research about atypical language development, especially in Romance languages. This book covers four main conditions causing atypical language development. Part I explores the linguistic and communicative characteristics of preterm children learning Romance languages. The focus of Part II centers on children with Specific Language Impairment. Hearing Loss in Part III is another relevant factor leading to atypical language development. The final part IV zeroes in on genetic syndromes coupled to cognitive impairment with special attention to language development. This book presents a much needed overview of the most recent findings in all relevant fields dealing with atypical language development in children speaking Romance languages.

This unique, edited book bridges studies in language disorders and linguistic theory with timely contributions from leading scholars in language development. It presents an attempt to define Specific Language Impairment, relating it to children of normal and disordered language capabilities. The chapter presentations examine language development across a variety of populations of children, from those with Specific Language Impairment to second language learners. The contributors discuss criteria for the definition of SLI, compare and contrast SLI with profiles of children with other disorders and dialects, and offer a comprehensive look at the Whole Human Language, which ties together spoken and signed languages. Methodological concerns that affect the credibility and generalizability of the findings are discussed and controversies between opposing linguistic approaches to language acquisition are presented. The conceptual thread that gradually reveals itself as the chapters unfold is a theoretical issue of central importance to cognitive theory, as well as to our understanding of the biological correlates of language--it concerns the variability that linguistic competence can manifest in children under different biological conditions and life circumstances. Language Competence Across Populations: Toward a Definition of Specific Language Impairment is an essential volume for advanced students and scholars in linguistics and psychology who have an interest in language acquisition and language disorders, as well as for the clinical professionals dealing with children with language impairments.